Auditory Neuropathy Spectrum Disorder
Overview
Hearing difficulties greater than would be expected from pure tone audiometry. The hearing difficulties are worse with speech compared with environmental sounds and are particularly affected by background noise.
Anatomy
It is characterised by normal outer hair cell (OHC) function but impaired neural transmission resulting in disruption of coding of acoustic signals in the auditory system.
Aetiology
Pathophysiology
Clinical Features
Investigations
Speech tests (in quiet and noise) worse than expected from audiometry.
Presence of OHC function as measured with cochlear microphonics (CM) and otoacoustic emissions (OAEs)
Absence or abnormality of the auditory brainstem response (ABR)
Management
Complications
Key Points
Auditory Processing Disorder
Overview
APD is diagnosed on the basis of the following criteria:
Normal audiometric thresholds in both ears
Abnormal performance in at least two validated auditory processing tests that assess different processes in at least one ear, including in a non-speech test
Presence of listening difficulties and/or risk factors associated with APD
Normal non-verbal intelligence
Good ability to follow test instructions
Anatomy
Aetiology
Neurological
Brain tumours
Stroke
De-myelinating conditions
Epilepsy
Prematurity/low birth weight
Higher Order Processing/Language
Higher order language:
Developmental disorders: Language impairment
Dyslexia
Higher order processing
ADHD, Autism, Etc
Spatial Processing disorder
Prolonged childhood history of chronic otitis media, can result in deficits to auditory processing